特殊人群肝豆状核变性诊治进展*

doi:10.3969/j.issn.1672-5069.2015.01.026

Abstract

Abstract: The clinical manifestations of Wilson's disease appear to be variable and it is sometimes difficult to diagnose at early stage. Although it is a genetic disorder of copper metabolism, if discovered early,effective treatments are available and the prognosis is good. The management of this disease in pregnant women, children and patient with acute liver failure,is highly concerned in clinical practice.

Key words: Wilson's disease, Diagnosis, Treatment, Acute liver failure

Cao Haixia, Fan Jiangao. What is special in patients with Wilson's disease in children and pregnant women[J]. JOURNAL OF PRACTICAL HEPATOLOGY, 2015, 18(1): 89-91.

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What is special in patients with Wilson's disease in children and pregnant women

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